Información del artículo
La etiopatogenia del síndrome o enfermedad de Behçet (EB) sigue siendo esquiva y sus manifestaciones clínicas, muy complejas, y genera una buena cantidad de artículos científicos. Por ejemplo, una búsqueda simple en PubMed muestra que en los últimos 5 años se han publicado 1.394 artículos, 159 de ellos revisiones. Además de los estudios básicos sobre etiopatogenia y mecanismos de la enfermedad, las diversas manifestaciones clínicas y sus tratamientos, también es fuente de debate la propia definición de la enfermedad, su clasificación y los criterios de clasificación y diagnóstico. En este artículo revisamos algunos aspectos en debate, así como las últimas alternativas terapéuticas y la situación de la EB en España.
Palabras clave:
Enfermedad de Behçet
Síndrome de Adamantiades-Behçet
Revisión
Behçet's disease/syndrome (BD) continues being aloof in his etiopathogenesis and very complex in its clinical manifestations. BD generates a good amount of scientific articles. For example, a simple search in PubMed sample that in the last 5 years has been published 1394 articles, 159 of them revisions. In addition to the basic studies on etiopahtogenesis and disease mechanisms, the diverse clinical manifestations and their treatments, also the own definition of the disease, its classification and the criteria of classification and diagnosis are debate source. In this article we reviewed some aspects in discussin as well as the last therapeutic alternatives and the situation of the EB in Spain.
Key words:
Behçet's disease/syndrome
Adamantiades-Behçet's disease
Review
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